Elevated liver glycogenolysis mediates higher blood glucose during acute exercise in Barth syndrome
Barth syndrome (BTHS) is an X-linked recessive genetic disorder due to mutations in the Tafazzin (TAFAZZIN) gene that russian z flag for sale lead to cardiac and skeletal muscle mitochondrial dysfunction.Previous studies in humans with BTHS demonstrate that the defects in muscle mitochondrial oxidative metabolism result in an enhanced reliance on a